| Q00 |
Anencephaly and similar malformations [+]
|
|
| Q00.0 |
Anencephaly
Acephaly
Acrania
Amyelencephaly
Hemianencephaly
Hemicephaly
|
| Q00.1 |
Craniorachischisis
|
| Q00.2 |
Iniencephaly
|
|
| Q01 |
Encephalocele [+]
| Includes: |
Arnold-Chiari syndrome, type III
encephalocystocele
encephalomyelocele
hydroencephalocele
hydromeningocele, cranial
meningocele, cerebral
meningoencephalocele
|
| Excludes 1: |
Meckel-Gruber syndrome (Q61.9)
|
|
|
| Q01.0 |
Frontal encephalocele
|
| Q01.1 |
Nasofrontal encephalocele
|
| Q01.2 |
Occipital encephalocele
|
| Q01.8 |
Encephalocele of other sites
|
| Q01.9 |
Encephalocele, unspecified
|
|
| Q02 |
Microcephaly
| Code first |
, if applicable, congenital Zika virus disease
|
| Includes: |
hydromicrocephaly
micrencephalon
|
| Excludes 1: |
Meckel-Gruber syndrome (Q61.9)
|
|
| Q03 |
Congenital hydrocephalus [+]
| Includes: |
hydrocephalus in newborn
|
| Excludes 1: |
Arnold-Chiari syndrome, type II (Q07.0-)
acquired hydrocephalus (G91.-)
hydrocephalus due to congenital toxoplasmosis (P37.1)
hydrocephalus with spina bifida (Q05.0-Q05.4)
|
|
|
| Q03.0 |
Malformations of aqueduct of Sylvius
Anomaly of aqueduct of Sylvius
Obstruction of aqueduct of Sylvius, congenital
Stenosis of aqueduct of Sylvius
|
| Q03.1 |
Atresia of foramina of Magendie and Luschka
Dandy-Walker syndrome
|
| Q03.8 |
Other congenital hydrocephalus
|
| Q03.9 |
Congenital hydrocephalus, unspecified
|
|
| Q04 |
Other congenital malformations of brain [+]
| Excludes 1: |
cyclopia (Q87.0)
macrocephaly (Q75.3)
|
|
|
| Q04.0 |
Congenital malformations of corpus callosum
Agenesis of corpus callosum
|
| Q04.1 |
Arhinencephaly
|
| Q04.2 |
Holoprosencephaly
|
| Q04.3 |
Other reduction deformities of brain
Absence of part of brain
Agenesis of part of brain
Agyria
Aplasia of part of brain
Hydranencephaly
Hypoplasia of part of brain
Lissencephaly
Microgyria
Pachygyria
| Excludes 1: |
congenital malformations of corpus callosum (Q04.0)
|
|
| Q04.4 |
Septo-optic dysplasia of brain
|
| Q04.5 |
Megalencephaly
|
| Q04.6 |
Congenital cerebral cysts
Porencephaly
Schizencephaly
| Excludes 1: |
acquired porencephalic cyst (G93.0)
|
|
| Q04.8 |
Other specified congenital malformations of brain
Arnold-Chiari syndrome, type IV
Macrogyria
|
| Q04.9 |
Congenital malformation of brain, unspecified
Congenital anomaly NOS of brain
Congenital deformity NOS of brain
Congenital disease or lesion NOS of brain
Multiple anomalies NOS of brain, congenital
|
|
| Q05 |
Spina bifida [+]
| Includes: |
hydromeningocele (spinal)
meningocele (spinal)
meningomyelocele
myelocele
myelomeningocele
rachischisis
spina bifida (aperta)(cystica)
syringomyelocele
|
| Use additional |
code for any associated paraplegia (paraparesis) (G82.2-) |
| Excludes 1: |
Arnold-Chiari syndrome, type II (Q07.0-)
spina bifida occulta (Q76.0)
|
|
|
| Q05.0 |
Cervical spina bifida with hydrocephalus
|
| Q05.1 |
Thoracic spina bifida with hydrocephalus
Dorsal spina bifida with hydrocephalus
Thoracolumbar spina bifida with hydrocephalus
|
| Q05.2 |
Lumbar spina bifida with hydrocephalus
Lumbosacral spina bifida with hydrocephalus
|
| Q05.3 |
Sacral spina bifida with hydrocephalus
|
| Q05.4 |
Unspecified spina bifida with hydrocephalus
|
| Q05.5 |
Cervical spina bifida without hydrocephalus
|
| Q05.6 |
Thoracic spina bifida without hydrocephalus
Dorsal spina bifida NOS
Thoracolumbar spina bifida NOS
|
| Q05.7 |
Lumbar spina bifida without hydrocephalus
Lumbosacral spina bifida NOS
|
| Q05.8 |
Sacral spina bifida without hydrocephalus
|
| Q05.9 |
Spina bifida, unspecified
|
|
| Q06 |
Other congenital malformations of spinal cord [+]
|
|
| Q06.0 |
Amyelia
|
| Q06.1 |
Hypoplasia and dysplasia of spinal cord
Atelomyelia
Myelatelia
Myelodysplasia of spinal cord
|
| Q06.2 |
Diastematomyelia
|
| Q06.3 |
Other congenital cauda equina malformations
|
| Q06.4 |
Hydromyelia
Hydrorachis
|
| Q06.8 |
Other specified congenital malformations of spinal cord
|
| Q06.9 |
Congenital malformation of spinal cord, unspecified
Congenital anomaly NOS of spinal cord
Congenital deformity NOS of spinal cord
Congenital disease or lesion NOS of spinal cord
|
|
| Q07 |
Other congenital malformations of nervous system [+]
| Excludes 2: |
congenital central alveolar hypoventilation syndrome (G47.35)
familial dysautonomia [Riley-Day] (G90.1)
neurofibromatosis (nonmalignant) (Q85.0-)
|
|
|
| Q07.0 |
Arnold-Chiari syndrome [+]
Arnold-Chiari syndrome, type II
| Excludes 1: |
Arnold-Chiari syndrome, type III (Q01.-)
Arnold-Chiari syndrome, type IV (Q04.8)
|
|
|
| Q07.00 |
Arnold-Chiari syndrome without spina bifida or hydrocephalus
|
| Q07.01 |
Arnold-Chiari syndrome with spina bifida
|
| Q07.02 |
Arnold-Chiari syndrome with hydrocephalus
|
| Q07.03 |
Arnold-Chiari syndrome with spina bifida and hydrocephalus
|
|
| Q07.8 |
Other specified congenital malformations of nervous system
Agenesis of nerve
Displacement of brachial plexus
Jaw-winking syndrome
Marcus Gunn's syndrome
|
| Q07.9 |
Congenital malformation of nervous system, unspecified
Congenital anomaly NOS of nervous system
Congenital deformity NOS of nervous system
Congenital disease or lesion NOS of nervous system
|
|