Neoplasms (C00-D49)

Note:
Functional activity
All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
Morphology [Histology]
Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
Primary malignant neoplasms overlapping site boundaries
A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
Malignant neoplasm of ectopic tissue
Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Malignant neoplasms of lip, oral cavity and pharynx (C00-C14)

C00 Malignant neoplasm of lip [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 1: malignant melanoma of lip (C43.0)
Merkel cell carcinoma of lip (C4A.0)
other and unspecified malignant neoplasm of skin of lip (C44.0-)
C01 Malignant neoplasm of base of tongue
Malignant neoplasm of dorsal surface of base of tongue
Malignant neoplasm of fixed part of tongue NOS
Malignant neoplasm of posterior third of tongue
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C02 Malignant neoplasm of other and unspecified parts of tongue [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C03 Malignant neoplasm of gum [+]
Includes: malignant neoplasm of alveolar (ridge) mucosa
malignant neoplasm of gingiva
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 2: malignant odontogenic neoplasms (C41.0-C41.1)
C04 Malignant neoplasm of floor of mouth [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C05 Malignant neoplasm of palate [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 1: Kaposi's sarcoma of palate (C46.2)
C06 Malignant neoplasm of other and unspecified parts of mouth [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional history of tobacco dependence (Z87.891)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C07 Malignant neoplasm of parotid gland
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C08 Malignant neoplasm of other and unspecified major salivary glands [+]
Includes: malignant neoplasm of salivary ducts
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 1: malignant neoplasms of specified minor salivary glands which are classified according to their anatomical location
Excludes 2: malignant neoplasms of minor salivary glands NOS (C06.9)
malignant neoplasm of parotid gland (C07)
C09 Malignant neoplasm of tonsil [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 2: malignant neoplasm of lingual tonsil (C02.4)
malignant neoplasm of pharyngeal tonsil (C11.1)
C10 Malignant neoplasm of oropharynx [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 2: malignant neoplasm of tonsil (C09.-)
C11 Malignant neoplasm of nasopharynx [+]
Use additional code to identify:
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C12 Malignant neoplasm of pyriform sinus
Malignant neoplasm of pyriform fossa
Use additional code to identify:
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
C13 Malignant neoplasm of hypopharynx [+]
Use additional code to identify:
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 2: malignant neoplasm of pyriform sinus (C12)
C14 Malignant neoplasm of other and ill-defined sites in the lip, oral cavity and pharynx [+]
Use additional code to identify:
Use additional alcohol abuse and dependence (F10.-)
Use additional exposure to environmental tobacco smoke (Z77.22)
Use additional exposure to tobacco smoke in the perinatal period (P96.81)
Use additional history of tobacco dependence (Z87.891)
Use additional occupational exposure to environmental tobacco smoke (Z57.31)
Use additional tobacco dependence (F17.-)
Use additional tobacco use (Z72.0)
Excludes 1: malignant neoplasm of oral cavity NOS (C06.9)

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