Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Excludes 2:
autoimmune disease (systemic) NOS (M35.9)
certain conditions originating in the perinatal period (P00-P96)
complications of pregnancy, childbirth and the puerperium (O00-O9A)
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
endocrine, nutritional and metabolic diseases (E00-E88)
human immunodeficiency virus [HIV] disease (B20)
injury, poisoning and certain other consequences of external causes (S00-T88)
neoplasms (C00-D49)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)

D65 Disseminated intravascular coagulation [defibrination syndrome]
Afibrinogenemia, acquired
Consumption coagulopathy
COVID-19 associated diffuse or disseminated intravascular coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic hemorrhage, acquired
Fibrinolytic purpura
Purpura fulminans
Code also , if applicable, associated condition
Excludes 1: disseminated intravascular coagulation (complicating):
abortion or ectopic or molar pregnancy (O00-O07, O08.1)
in newborn (P60)
pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D66 Hereditary factor VIII deficiency
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A
Excludes 1: factor VIII deficiency with vascular defect (D68.0-)
D67 Hereditary factor IX deficiency
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
D68 Other coagulation defects [+]
Excludes 1: abnormal coagulation profile NOS (R79.1)
Excludes 2: coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D69 Purpura and other hemorrhagic conditions [+]
Excludes 1: benign hypergammaglobulinemic purpura (D89.0)
cryoglobulinemic purpura (D89.1)
essential (hemorrhagic) thrombocythemia (D47.3)
hemorrhagic thrombocythemia (D47.3)
purpura fulminans (D65)
thrombotic thrombocytopenic purpura (M31.19)
Waldenström hypergammaglobulinemic purpura (D89.0)

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