Diseases of the nervous system (G00-G99)
Excludes 2:
certain conditions originating in the perinatal period (P04-P96) certain infectious and parasitic diseases (A00-B99) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Demyelinating diseases of the central nervous system (G35-G37)
G35
Multiple sclerosis [+]
G35.A
Relapsing-remitting multiple sclerosis
Excludes 1:
demyelinating disease of central nervous system, unspecified (G37.9)
G35.B
Primary progressive multiple sclerosis [+]
G35.B0
Primary progressive multiple sclerosis, unspecified
G35.B1
Active primary progressive multiple sclerosis Primary progressive multiple sclerosis with evidence of inflammatory disease activity
G35.B2
Non-active primary progressive multiple sclerosis Primary progressive multiple sclerosis without evidence of inflammatory disease activity
G35.C
Secondary progressive multiple sclerosis [+]
G35.C0
Secondary progressive multiple sclerosis, unspecified
G35.C1
Active secondary progressive multiple sclerosis Secondary progressive multiple sclerosis with evidence of inflammatory disease activity
G35.C2
Non-active secondary progressive multiple sclerosis Secondary progressive multiple sclerosis without evidence of inflammatory disease activity
G35.D
Multiple sclerosis, unspecified Disseminated multiple sclerosis Generalized multiple sclerosis Multiple sclerosis NOS Multiple sclerosis of brain stem Multiple sclerosis of cord
G36
Other acute disseminated demyelination [+]
Excludes 1:
postinfectious encephalitis and encephalomyelitis NOS (G04.01)
G36.0
Neuromyelitis optica [Devic] Demyelination in optic neuritis
Excludes 2:
optic neuritis NOS (H46)
G36.1
Acute and subacute hemorrhagic leukoencephalitis [Hurst]
G36.8
Other specified acute disseminated demyelination
G36.9
Acute disseminated demyelination, unspecified
G37
Other demyelinating diseases of central nervous system [+]
G37.0
Diffuse sclerosis of central nervous system Periaxial encephalitis Schilder's disease
Excludes 1:
X linked adrenoleukodystrophy (E71.52-)
G37.1
Central demyelination of corpus callosum
G37.2
Central pontine myelinolysis
G37.3
Acute transverse myelitis in demyelinating disease of central nervous system Acute transverse myelitis NOS Acute transverse myelopathy
Excludes 1:
acute flaccid myelitis (G04.82) multiple sclerosis (G35-) neuromyelitis optica [Devic] (G36.0)
G37.4
Subacute necrotizing myelitis of central nervous system
G37.5
Concentric sclerosis [Balo] of central nervous system
G37.8
Other specified demyelinating diseases of central nervous system [+]
G37.81
Myelin oligodendrocyte glycoprotein antibody disease MOG antibody disease
Code also
associated manifestations, if known, such as: noninfectious acute disseminated encephalomyelitis (G04.81) neuromyelitis optica (G36.0)
G37.89
Other specified demyelinating diseases of central nervous system
G37.9
Demyelinating disease of central nervous system, unspecified Clinically isolated syndromes
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The ICD-10 Diagnosis Codes are based on the latest diagnosis coding files (2027 ICD-10-CM and 2018 GEMs ).
The ICD-10 Procedure Codes are based on the latest procedure coding files (2027 ICD-10-PCS and 2018 GEMs ).