Diseases of the circulatory system (I00-I99)

Excludes 2:
certain conditions originating in the perinatal period (P04-P96)
certain infectious and parasitic diseases (A00-B99)
complications of pregnancy, childbirth and the puerperium (O00-O9A)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
endocrine, nutritional and metabolic diseases (E00-E88)
injury, poisoning and certain other consequences of external causes (S00-T88)
neoplasms (C00-D49)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
systemic connective tissue disorders (M30-M36)
transient cerebral ischemic attacks and related syndromes (G45.-)

Other forms of heart disease (I30-I5A)

I30 Acute pericarditis [+]
Includes: acute mediastinopericarditis
acute myopericarditis
acute pericardial effusion
acute pleuropericarditis
acute pneumopericarditis
Excludes 1: Dressler's syndrome (I24.1)
rheumatic pericarditis (acute) (I01.0)
viral pericarditis due to Coxsakie virus (B33.23)
I31 Other diseases of pericardium [+]
Excludes 1: diseases of pericardium specified as rheumatic (I09.2)
postcardiotomy syndrome (I97.0)
traumatic injury to pericardium (S26.-)
I32 Pericarditis in diseases classified elsewhere
Code first underlying disease
Excludes 1: pericarditis (in):
coxsackie (virus) (B33.23)
gonococcal (A54.83)
meningococcal (A39.53)
rheumatoid (arthritis) (M05.31)
syphilitic (A52.06)
systemic lupus erythematosus (M32.12)
tuberculosis (A18.84)
I33 Acute and subacute endocarditis [+]
Excludes 1: acute rheumatic endocarditis (I01.1)
endocarditis NOS (I38)
I34 Nonrheumatic mitral valve disorders [+]
Excludes 1: mitral valve disease (I05.9)
mitral valve failure (I05.8)
mitral valve stenosis (I05.0)
mitral valve disorder of unspecified cause with diseases of aortic and/or tricuspid valve(s) (I08.-)
mitral valve disorder of unspecified cause with mitral stenosis or obstruction (I05.0)
mitral valve disorder specified as congenital (Q23.2, Q23.9)
mitral valve disorder specified as rheumatic (I05.-)
I35 Nonrheumatic aortic valve disorders [+]
Excludes 1: aortic valve disorder of unspecified cause but with diseases of mitral and/or tricuspid valve(s) (I08.-)
aortic valve disorder specified as congenital (Q23.0, Q23.1)
aortic valve disorder specified as rheumatic (I06.-)
hypertrophic subaortic stenosis (I42.1)
I36 Nonrheumatic tricuspid valve disorders [+]
Excludes 1: tricuspid valve disorders of unspecified cause (I07.-)
tricuspid valve disorders specified as congenital (Q22.4, Q22.8, Q22.9)
tricuspid valve disorders specified as rheumatic (I07.-)
tricuspid valve disorders with aortic and/or mitral valve involvement (I08.-)
I37 Nonrheumatic pulmonary valve disorders [+]
Excludes 1: pulmonary valve disorder specified as congenital (Q22.1, Q22.2, Q22.3)
pulmonary valve disorder specified as rheumatic (I09.89)
I38 Endocarditis, valve unspecified
Includes: endocarditis (chronic) NOS
valvular incompetence NOS
valvular insufficiency NOS
valvular regurgitation NOS
valvular stenosis NOS
valvulitis (chronic) NOS
Excludes 1: congenital insufficiency of cardiac valve NOS (Q24.8)
congenital stenosis of cardiac valve NOS (Q24.8)
endocardial fibroelastosis (I42.4)
endocarditis specified as rheumatic (I09.1)
I39 Endocarditis and heart valve disorders in diseases classified elsewhere
Code first underlying disease, such as:
Q fever (A78)
Excludes 1: endocardial involvement in:
candidiasis (B37.6)
gonococcal infection (A54.83)
Libman-Sacks disease (M32.11)
listerosis (A32.82)
meningococcal infection (A39.51)
rheumatoid arthritis (M05.31)
syphilis (A52.03)
tuberculosis (A18.84)
typhoid fever (A01.02)
I40 Acute myocarditis [+]
Includes: subacute myocarditis
Excludes 1: acute rheumatic myocarditis (I01.2)
I41 Myocarditis in diseases classified elsewhere
Code first underlying disease, such as:
typhus (A75.0-A75.9)
Excludes 1: myocarditis (in):
Chagas' disease (chronic) (B57.2)
acute (B57.0)
coxsackie (virus) infection (B33.22)
diphtheritic (A36.81)
gonococcal (A54.83)
influenzal (J09.X9, J10.82, J11.82)
meningococcal (A39.52)
mumps (B26.82)
rheumatoid arthritis (M05.31)
sarcoid (D86.85)
syphilis (A52.06)
toxoplasmosis (B58.81)
tuberculous (A18.84)
I42 Cardiomyopathy [+]
Code first pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)
Includes: myocardiopathy
Excludes 2: ischemic cardiomyopathy (I25.5)
peripartum cardiomyopathy (O90.3)
ventricular hypertrophy (I51.7)
I43 Cardiomyopathy in diseases classified elsewhere
Code first underlying disease, such as:
amyloidosis (E85.-)
glycogen storage disease (E74.0-)
gout (M10.0-)
thyrotoxicosis (E05.0-E05.9-)
Excludes 1: cardiomyopathy (in):
coxsackie (virus) (B33.24)
diphtheria (A36.81)
sarcoidosis (D86.85)
tuberculosis (A18.84)
I44 Atrioventricular and left bundle-branch block [+]
I45 Other conduction disorders [+]
I46 Cardiac arrest [+]
Excludes 2: cardiogenic shock (R57.0)
I47 Paroxysmal tachycardia [+]
Code first tachycardia complicating:
abortion or ectopic or molar pregnancy (O00-O07, O08.8)
obstetric surgery and procedures (O75.4)
Excludes 1: tachycardia NOS (R00.0)
sinoauricular tachycardia NOS (R00.0)
sinus [sinusal] tachycardia NOS (R00.0)
I48 Atrial fibrillation and flutter [+]
I49 Other cardiac arrhythmias [+]
Code first cardiac arrhythmia complicating:
abortion or ectopic or molar pregnancy (O00-O07, O08.8)
obstetric surgery and procedures (O75.4)
Excludes 1: neonatal dysrhythmia (P29.1-)
sinoatrial bradycardia (R00.1)
sinus bradycardia (R00.1)
vagal bradycardia (R00.1)
Excludes 2: bradycardia NOS (R00.1)
I50 Heart failure [+]
Code first heart failure complicating abortion or ectopic or molar pregnancy (O00-O07, O08.8)
heart failure due to hypertension (I11.0)
heart failure due to hypertension with chronic kidney disease (I13.-)
heart failure following surgery (I97.13-)
obstetric surgery and procedures (O75.4)
rheumatic heart failure (I09.81)
Excludes 2: cardiac arrest (I46.-)
neonatal cardiac failure (P29.0)
I51 Complications and ill-defined descriptions of heart disease [+]
Excludes 1: any condition in I51.4-I51.9 due to hypertension (I11.-)
any condition in I51.4-I51.9 due to hypertension and chronic kidney disease (I13.-)
heart disease specified as rheumatic (I00-I09)
I52 Other heart disorders in diseases classified elsewhere
Code first underlying disease, such as:
congenital syphilis (A50.5)
mucopolysaccharidosis (E76.3)
schistosomiasis (B65.0-B65.9)
Excludes 1: heart disease (in):
gonococcal infection (A54.83)
meningococcal infection (A39.50)
rheumatoid arthritis (M05.31)
syphilis (A52.06)
I5A Non-ischemic myocardial injury (non-traumatic)
Acute (non-ischemic) myocardial injury
Chronic (non-ischemic) myocardial injury
Unspecified (non-ischemic) myocardial injury
Code first the underlying cause, if known and applicable, such as:
acute kidney failure (N17.-)
acute myocarditis (I40.-)
cardiomyopathy (I42.-)
chronic kidney disease (CKD) (N18.-)
heart failure (I50.-)
hypertensive urgency (I16.0)
nonrheumatic aortic valve disorders (I35.-)
paroxysmal tachycardia (I47.-)
pulmonary embolism (I26.-)
pulmonary hypertension (I27.0, I27.2-)
sepsis (A41.-)
takotsubo syndrome (I51.81)
Excludes 1: acute myocardial infarction (I21.-)
injury of heart (S26.-)
Excludes 2: other acute ischemic heart diseases (I24.-)

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